The condition is characterized by an overgrowth of bone hyperostosis in the facial and cranial bones. The neglect of examining the entire skeleton roentgenologically would account, in many instances, for the idea that leontiasis ossea is a monostotic disease. Suggested case of langerhans cell histiocytosis in a. Chiari type i malformation caused by craniometaphyseal dysplasia masato tanaka, shinya arataki,yoshihisa sugimoto, tomoyuki takigawa, tomoko tetsunaga, and toshifumi ozaki department of orthopaedic surgery, okayama university hospital, okayama 7008558, japan. A case of leontiasis ossea which was primarily investigated as a result of oral findings is presented. Leontiasis ossea definition of leontiasis ossea by. Leontiasis ossea, flail chest and pancytopenia in a patient with renal osteodystrophy. Histological and biochemical testing can provide further differentiation from. Aug 15, 2006 leontiasis ossea leonine facies or cervical canal stenosis are rare complications of polyostotic fibrous dysplasia pfd. Fatal uremic leontiasis ossea in longlasting uncontrolled. Leontiasis ossea leonine facies or cervical canal stenosis are rare complications of polyostotic fibrous dysplasia pfd. Thickening of the inner table of the frontal bone, which may be associated with hypertrichosis and obesityit most commonly affects women near menopause. Leontiasis ossea is a rare medical condition which is characterized by an overgrowth of the facial and cranial bones secondary to chronic. Leontiasis ossea definition of leontiasis ossea by the.
If routine skeletal xrays were made, one might then have a better opinion as to the category into which each case of leontiasis ossea might fall. Leontiasis ossea generalisata definition of leontiasis. In one of his classic lectures delivered during the winter semester 18621863 at the university of berlin, virchow 1 directed special attention to the hyperostoses affecting the facial and cranial bones. Leontiasis ossea synonyms, leontiasis ossea pronunciation, leontiasis ossea translation, english dictionary definition of leontiasis ossea. In one of his classic lectures delivered during the winter semester 18621863 at the university of berlin, virchow1 directed special attention to the hyperostos. This case report documents dramatic leontiasis ossea in pfd as well as post traumatic cervical cord contusion due to hyperextension injury in a patient with generalized pfd involving the craniofacial bones, axial skeleton and entire spine with secondary cervical canal. Leontiasis ossea and post traumatic cervical cord contusion. Get a printable copy pdf file of the complete article 629k, or click on a page image below to browse page by page.
What links here related changes upload file special pages permanent link page. It is not a disease in itself, but a symptom of other diseases, including pagets disease, fibrous dysplasia, hyperparathyroidism and renal osteodystrophy. The ectoparasitosis is associated with poverty and occurs in many resource. Leontiasis ossea definition of leontiasis ossea by the free. Uremic leontiasis ossea, a rare presentation of severe. Leontiasis ossea following secondary hyperparathyroidism. Extensive bone growth with demineralization was noted on the mandible, suggesting uremic leontiasis ossea. The thorax, both shoulder joints and vertebrae showed diffuse osteosclerotic and osteolyitic changes fig.
Skull with leontiasis ossea, also commonly known as lion face. Supplements of calcium and vitamin d combined with reduction of phosphate levels have been recommended to be effective. Renal osteodystrophy is a common complication of endstage renal failure patients. Leontiasis ossea is a rare condition which is characterized by an overgrowth of the facial bones. The first is an alteration of the long bones in the metaphyseal regions similar to, but less severe than, the changes seen in metaphyseal dysplasia or pyle disease. Uniqueness of radiographic patterns of the frontal sinus for personal identification neha patil, freny r. Leontiasis ossea is a rare medical condition, with characteristic overgrowth of the facial and cranial bones. Ronald perlman born april, 1950 is an american actor and voice actor. Leontiasis ossea, also known as leontiasis, lion face or lion face syndrome, is a rare medical condition, characterized by an overgrowth of the facial and cranial bones. Get a printable copy pdf file of the complete article 457k, or click on a page image below to browse page by page. Tungiasis is a parasitic skin disease caused by the female sand flea tunga penetrans, which burrows into the skin, usually on the feet. A 36yearold man with chronic kidney disease ckd, undergoing hemodialysis therapy since 16yearold, was referred to our hospital for the. Leontiasis ossea, also known as lion face syndrome and leontiasis is a rare medical condition which is described as an overgrowth of the facial and cranial bones. Facial skeletal changes associated with hyperparathyroidism assume three radiographic patterns.
Uremic leontiasis ossea, a rare presentation of severe renal. He dwelt at length on this localization of bone hypertrophy because it served him well in the. Chest computed tomography ct revealed diffuse fluffy groundglass centrilobular opacities with calcifications in the right lung. Chiari type i malformation caused by craniometaphyseal dysplasia masato tanaka, shinya arataki,yoshihisa sugimoto, tomoyuki takigawa, tomoko tetsunaga, and toshifumi ozaki. Its not a disease, but rather a symptom of different diseases such as pagets disease, hyperparathyroidism, fibrous dysplasia, syphilitic osteoperiostitis and renal osteodystrophy. Files are available under licenses specified on their description page. Leontiasis ossea, also known as leontiasis, lion face or lion face syndrome, is a rare medical. This rare condition is symptomatic of several diseases including fibrous dysplasia, pagets disease, hyperparathyroidism, syphilitic osteoperiostitis and renal osteodystrophy. The golden army 2008, and clay morrow on the television series sons of anarchy 200820. Since much of the biological history of every living creature is shaped by its diseases, recognizing them in fossilized bone can. Karjodkar, subodh sontakke, kaustubh sansare, and rohini salvi department of oral medicine and radiology, mgm, dental college and hospital, navi mumbai, india. It is not a disease in itself, but a symptom of other diseases, including pagets disease, fibrous dysplasia, hyperparathyroidism and renal osteodystrophy, and is also. In one of his classic lectures delivered during the winter semester 18621863 at the university of berlin, virchow1 directed special attention to the hyperostoses affecting the facial and cranial bones. This case report documents dramatic leontiasis ossea in pfd as well as post traumatic cervical cord contusion due to hyperextension injury in a patient with generalized pfd involving the craniofacial bones, axial skeleton and entire spine with.
Leontiasis ossea is believed to be the rarest and manifests clinically as widening of the interdental spaces, flattening of the nares and nasal bridge, and jaw enlargement. Leontiasis ossea, also known as leontiasis or lion face, is a rare medical condition, characterized by an overgrowth of the facial and cranial bones. Virgilio ferruccio ferrario, chiarella sforza, claudia dellavia, andrea galassi, and diego brancaccio 2005 abnormal variations in the facial soft tissues of adult uremic patients on chronic dialysis. Although it is most frequently associated with craniofacial fibrous dysplasia, it has a broader meaning encompassing other lesions that have similar appearance 1,4 the distinction is made between true leontiasis ossea craniofacial. Total parathyroidectomy with autotransplantation for a rare disease derived from uremic secondary hyperparathyroidism, the uremic leontiasis ossea. Leontiasis ossea following secondary hyperparathyroidism and. A case of leontiasis ossea, observed over a period of fifty years, is described with particular reference to certain similarities and differences as compared with pagets disease of bone osteitis. Cattaneo museum, institute of human anatomy, bologna lion facies. If you do not see its contents the file may be temporarily unavailable at the journal website or you do not have a pdf plugin installed and enabled in your browser. Mr and ct findings of cyst degeneration of sphenoid bone. Although it is most frequently associated with craniofacial fibrous dysplasia, it has a br. Media in category osteopathies the following 27 files are in this category, out of 27 total.
Paget disease of the bone presenting as leontiasis ossea. Leontiasis ossea is a term that can be used to describe the progressive hypertrophy of facial and cranial bones associated with a group of diseases, including paget disease and. There are present atypical features which leave the diagnosis between the pathologic entity described as leontiasis ossea and the clinical appearance known as leontiasis ossea the latter of which may be due to a number of underlying causes. Definition the term myiasis was first proposed by hope 1840 to refer to the diseases of humans originating specifically with dipterous larvae, as. This case report documents dramatic leontiasis ossea in pfd as well as post traumatic cervical cord contusion due to hyperextension injury in a. Report of 2 cases with an emphasis on panoramic imaging features hangyeol yeom 1. Chiari type i malformation caused by craniometaphyseal dysplasia. He played the role of vincent on the television series beauty and the beast 19871990, for which he won a golden globe award, the comic book character hellboy in both hellboy 2004 and its sequel hellboy ii. Get a printable copy pdf file of the complete article 885k, or click on a page image below to browse page by page. Media in category leontiasis ossea the following 3 files are in this category, out of 3 total. Since much of the biological history of every living creature is shaped by its. Leontiasis ossea lion face syndrome medigoo health. Meaning of leontiasis ossea generalisata medical term. Leontiasis ossea is a term that can be used to describe the progressive hypertrophy of facial and cranial bones associated with a group of diseases, including paget disease and fibrous dysplasia.
He dwelt at length on this localization of bone hypertrophy because it served him well in the discussion of the general subject of periostosis and hyperostosis. Wnt signaling and bone thenamewntwasintroducedalmost30yearsagoreferring to the winglesstype mouse mammary tumor virus integration. Full text full text is available as a scanned copy of the original print version. Leontiasis ossea, flail chest and pancytopenia in a. Lateral wall and basal septum of left ventricle lv were radioopaque, suggesting calcified myocardium fig. Leontiasis ossea is a rare medical condition which is characterized by an overgrowth of the facial and cranial bones secondary to chronic renal failure and secondary hyperparathyroidism. Abnormal variations in the facial soft tissues of adult. This case report documents dramatic leontiasis ossea in pfd as well as post traumatic cervical cord contusion due to hyperextension. Soft tissue tunneling through the residual osseous matrix remains a key imaging finding. Leontiasis ossea is largely a historical term used to describe a number of conditions that result in the affected patients face resembling that of a lion. Ch 8 nonneoplastic diseases of bone flashcards quizlet.
Its most severe osseous complication is characterized by massive thickening of the cranial vault and facial bones, called uremic leontiasis ossea ulo, with only few cases reported in the literature. Leontiasis ossea definition of leontiasis ossea by medical. Links to pubmed are also available for selected references. Leontiasis ossea in a patient with hyperparathyroidism secondary to chronic renal failure. Several radiologic patterns of maxillofacial involvement have been described in the setting of renal osteodystrophy.
Dec 01, 2017 1,2 the term leontiasis ossea has been generalized to describe the appearance of craniofacial hypertrophy in the setting of many diseasespaget disease, fibrous dysplasia, reactive inflammatory bone disease, renal osteodystrophywhich result in leonine facies. Looking for online definition of leontiasis ossea generalisata in the medical dictionary. Susceptibility to diseases is common to humans and dinosaurs. Any information contained in this pdf file is automatically generated from digital material submitted to epos by third parties in the form of scientific presentations. Jun 01, 2015 leontiasis ossea, also known as leontiasis or lion face, is a rare medical condition, characterized by an overgrowth of the facial and cranial bones. Chiari type i malformation caused by craniometaphyseal. Cystic change is rare in fibrous dysplasia fd, especially in mccunealbright syndrome. Leontiasis ossea and post traumatic cervical cord contusion in.
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